J Korean Cleft Palate-Craniofac Assoc Search

CLOSE


Journal of Korean Cleft Palate-Craniofacial Association 2005;6(2):133-135.
A Case of Severe Scleroderma en Coup de Sabre with Ipsilateral Body Atrophy.
So Min Hwang, Chul Sun Kang, David J David
1Aesthetic, Plastic and Reconstructive Surgery Center, Good Moonhwa Hospital, Busan, Korea. smhwang@moon hwa.or.kr
2Australian Craniofacial Unit, Women's & Children's Hospital, Adelaide, Australia.
Abstract
Linear scleroderma is a variant of localized scleroderma which may occur in the head, trunk and extremities, affecting variously the skin, subcutaneous tissue, muscle, cartilage and bone. Particularly, scleroderma en coup de sabre is the descriptive term denoting linear scleroderma of the frontoparietal area of the scalp and face. We report a case of severe scleroderma en coup de sabre with ipsilateral body atrophy(total hemiatrophy) who underwent multidisciplinary assessment and required both two-jaw surgery and groin free flap to correct the underlying skeletal deformities and augment the facial soft tissues. The reason for classifying this as a case of scleroderma en coup de sabre in preference to Parry-Romberg syndrome is because of the striking clinical features seen in this patient.
Keywords: Scleroderma; Hemifacial atrophy; Total hemiatrophy; Two-jaw surgery; Groin free flap
TOOLS
  • PDF Links   PDF Links
  • Full text via DOI   Full text via DOI
  • Cited  Cited
    Cited
    export Copy
    Close
Share :
Facebook Twitter Linked In Google+ Line it
METRICS Graph View
  • 1,381 View
  • 0 Download
Related articles in ACFS


ABOUT
ARTICLE CATEGORY

Browse all articles >

BROWSE ARTICLES
AUTHOR INFORMATION
Editorial Office
Dept. of Plastic and Reconstructive Surgery Chonnam National University Medical School, 42 Jebong-ro, Dong-gu, Gwangju 61469, Korea
Tel: +82-62-220-6354    Fax: +82-62-220-6357    E-mail: office_acfs@kcpca.or.kr                

Copyright © 2024 by Korean Cleft Palate-Craniofacial Association.

Developed in M2PI

Close layer
prev next